TAFA1

Chr 3

TAFA chemokine like family member 1

Also known as: FAM19A1, TAFA-1

This gene encodes a small secreted protein that functions as a brain-specific chemokine and serves as a ligand for CMKLR2, regulating neural stem cell proliferation and differentiation. Mutations in TAFA1 cause autosomal recessive developmental and epileptic encephalopathy characterized by severe intellectual disability, refractory seizures, and brain malformations. The pathogenic mechanism appears to involve loss of function of this secreted regulatory factor critical for normal brain development.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.74
Clinical SummaryTAFA1
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.23) despite low pLI — interpret in context.
📋
ClinVar Variants
11 unique Pathogenic / Likely Pathogenic· 24 VUS of 38 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.74LOEUF
pLI 0.331
Z-score 2.07
OE 0.23 (0.100.74)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.92Z-score
OE missense 0.71 (0.570.89)
57 obs / 80.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.23 (0.100.74)
00.351.4
Missense OE0.71 (0.570.89)
00.61.4
Synonymous OE1.05
01.21.6
LoF obs/exp: 2 / 8.5Missense obs/exp: 57 / 80.2Syn Z: -0.19

ClinVar Variant Classifications

38 submitted variants in ClinVar

Classification Summary

Pathogenic10
Likely Pathogenic1
VUS24
Conflicting2
10
Pathogenic
1
Likely Pathogenic
24
VUS
2
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
10
0
10
Likely Pathogenic
0
0
1
0
1
VUS
0
15
9
0
24
Likely Benign
0
0
0
0
0
Benign
0
0
0
0
0
Conflicting
2
Total01520037

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

TAFA1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 2 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found