TAF7L

Chr X

TATA-box binding protein associated factor 7 like

Also known as: CT40, TAF2Q

The protein functions as a spermatogenesis-specific component of the DNA-binding general transcription factor complex TFIID, which mediates promoter responses to various transcriptional activators and repressors. Mutations cause male infertility due to impaired spermatogenesis, following an autosomal recessive inheritance pattern. The gene is highly constrained against loss-of-function variants, indicating that complete loss of protein function is likely pathogenic.

Summary from RefSeq, UniProt
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0
Active trials
3
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.27
LOEUF· LoF intol.
LOF
Mechanism· predicted
Clinical SummaryTAF7L
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.99). One damaged copy is likely sufficient to cause disease.
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.27LOEUF
pLI 0.986
Z-score 3.64
OE 0.06 (0.020.27)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
0.14Z-score
OE missense 0.97 (0.851.10)
169 obs / 174.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.06 (0.020.27)
00.351.4
Missense OE0.97 (0.851.10)
00.61.4
Synonymous OE0.88
01.21.6
LoF obs/exp: 1 / 17.4Missense obs/exp: 169 / 174.4Syn Z: 0.76
DN
0.3991th %ile
GOF
0.15100th %ile
LOF
0.64top 25%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.27

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TAF7L · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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