TAF4B

Chr 18AR

TATA-box binding protein associated factor 4b

Also known as: SPGF13, TAF2C2, TAFII105

TAF4B encodes a cell type-specific subunit of the TFIID transcription factor complex that functions as a gene-selective coactivator, particularly in B cells, and plays roles in spermiogenesis and oogenesis. Biallelic mutations cause spermatogenic failure with autosomal recessive inheritance. The gene shows high constraint against loss-of-function variants (LOEUF 0.41), suggesting intolerance to complete protein loss.

Summary from RefSeq, OMIM, UniProt
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Primary Disease Associations & Inheritance

?Spermatogenic failure 13MIM #615841
AR
0
Active trials
3
Pubs (1 yr)
38
P/LP submissions
0%
P/LP missense
0.41
LOEUF
Mechanism
Clinical SummaryTAF4B
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.24) despite low pLI — interpret in context.
📋
ClinVar Variants
36 unique Pathogenic / Likely Pathogenic· 127 VUS of 226 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.41LOEUF
pLI 0.234
Z-score 4.37
OE 0.24 (0.140.41)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.35Z-score
OE missense 0.95 (0.881.03)
417 obs / 437.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.24 (0.140.41)
00.351.4
Missense OE0.95 (0.881.03)
00.61.4
Synonymous OE1.12
01.21.6
LoF obs/exp: 9 / 38.1Missense obs/exp: 417 / 437.8Syn Z: -1.26

ClinVar Variant Classifications

226 submitted variants in ClinVar

Classification Summary

Pathogenic35
Likely Pathogenic1
VUS127
Likely Benign15
Benign13
35
Pathogenic
1
Likely Pathogenic
127
VUS
15
Likely Benign
13
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
35
0
35
Likely Pathogenic
0
0
1
0
1
VUS
0
119
8
0
127
Likely Benign
0
8
2
5
15
Benign
0
7
1
5
13
Total01344710191

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

TAF4B · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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