TAF13

Chr 1

TATA-box binding protein associated factor 13

Also known as: MRT60, TAF(II)18, TAF2K, TAFII-18, TAFII18

Initiation of transcription by RNA polymerase II requires the activities of more than 70 polypeptides. The protein that coordinates these activities is transcription factor IID (TFIID), which binds to the core promoter to position the polymerase properly, serves as the scaffold for assembly of the remainder of the transcription complex, and acts as a channel for regulatory signals. TFIID is composed of the TATA-binding protein (TBP) and a group of evolutionarily conserved proteins known as TBP-associated factors or TAFs. TAFs may participate in basal transcription, serve as coactivators, function in promoter recognition or modify general transcription factors (GTFs) to facilitate complex assembly and transcription initiation. This gene encodes a small subunit associated with a subset of TFIID complexes. This subunit interacts with TBP and with two other small subunits of TFIID, TAF10 and TAF11. There is a pseudogene located on chromosome 6. [provided by RefSeq, Jul 2008]

ResearchGenerating clinical summary…
DNmechanismLOEUF 1.08
Clinical SummaryTAF13
Population Constraint (gnomAD)
Low constraint (pLI 0.02) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
4 unique Pathogenic / Likely Pathogenic· 8 VUS of 19 total submissions
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.08LOEUF
pLI 0.016
Z-score 1.41
OE 0.47 (0.231.08)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
1.26Z-score
OE missense 0.55 (0.420.73)
35 obs / 63.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.47 (0.231.08)
00.351.4
Missense OE?0.55 (0.420.73)
00.61.4
Synonymous OE?1.24
01.21.6
LoF obs/exp: 4 / 8.4Missense obs/exp: 35 / 63.2Syn Z: -0.83
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
strongTAF13-related intellectual disability and microcephalyOTHERAR

This gene — mechanism propensity

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.7327th %ile
GOF
0.4578th %ile
LOF
0.3648th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

19 submitted variants in ClinVar

Classification Summary

Pathogenic1
Likely Pathogenic3
VUS8
Likely Benign3
Benign1
1
Pathogenic
3
Likely Pathogenic
8
VUS
3
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
1
0
0
1
Likely Pathogenic
1
1
1
0
3
VUS
1
6
1
0
8
Likely Benign
0
0
1
2
3
Benign
0
0
1
0
1
Total284216

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

14 pathogenic / likely-pathogenic (of 33) ClinVar copy-number / structural variants overlap TAF13 — these span large chromosomal regions, not the gene specifically, and are excluded from the counts above. Explore in CNV tools →

Protein Context — Lollipop Plot

TAF13 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →