TADA2B

Chr 4

transcriptional adaptor 2B

Also known as: ADA2(beta), ADA2B

TADA2B encodes a transcriptional adaptor protein that coordinates histone acetyltransferase activity and links transcription factors to basal transcriptional machinery. Mutations cause intellectual disability with speech delay and dysmorphic facies, inherited in an autosomal dominant pattern. The gene shows high constraint against loss-of-function variants, suggesting intolerance to haploinsufficiency.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
3
Pubs (1 yr)
84
P/LP submissions
0%
P/LP missense
0.49
LOEUF
Mechanism
Clinical SummaryTADA2B
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.72) — some intolerance to loss-of-function variants.
📋
ClinVar Variants
84 unique Pathogenic / Likely Pathogenic· 33 VUS of 120 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.49LOEUF
pLI 0.724
Z-score 2.82
OE 0.15 (0.060.49)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.80Z-score
OE missense 0.52 (0.450.59)
136 obs / 263.8 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.15 (0.060.49)
00.351.4
Missense OE0.52 (0.450.59)
00.61.4
Synonymous OE1.05
01.21.6
LoF obs/exp: 2 / 12.9Missense obs/exp: 136 / 263.8Syn Z: -0.39

ClinVar Variant Classifications

120 submitted variants in ClinVar

Classification Summary

Pathogenic80
Likely Pathogenic4
VUS33
Likely Benign1
80
Pathogenic
4
Likely Pathogenic
33
VUS
1
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
80
0
80
Likely Pathogenic
0
0
4
0
4
VUS
0
30
3
0
33
Likely Benign
0
1
0
0
1
Benign
0
0
0
0
0
Total031870118

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

TADA2B · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 2 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found