SYT10 encodes a calcium sensor protein that specifically regulates calcium-dependent exocytosis of IGF1-containing secretory vesicles in olfactory bulb neurons, which is required for normal smell perception. The gene is not highly constrained against loss-of-function variants (pLI = 0.00006), and no established human disease phenotypes have been reported for SYT10 mutations to date.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
2
Pubs (1 yr)
14
P/LP submissions
0%
P/LP missense
0.75
LOEUF
Multiple*
Mechanism· predicted
Clinical SummarySYT10
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
14 unique Pathogenic / Likely Pathogenic· 76 VUS of 100 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.75LOEUF
pLI 0.000
Z-score 2.48
OE 0.45 (0.280.75)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.45Z-score
OE missense 0.92 (0.841.02)
265 obs / 286.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.45 (0.280.75)
00.351.4
Missense OE0.92 (0.841.02)
00.61.4
Synonymous OE0.95
01.21.6
LoF obs/exp: 11 / 24.2Missense obs/exp: 265 / 286.5Syn Z: 0.37
DN
0.81top 10%
GOF
0.77top 25%
LOF
0.3261th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

100 submitted variants in ClinVar

Classification Summary

Pathogenic14
VUS76
Likely Benign1
Benign2
Conflicting1
14
Pathogenic
76
VUS
1
Likely Benign
2
Benign
1
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
14
0
14
Likely Pathogenic
0
0
0
0
0
VUS
0
73
3
0
76
Likely Benign
0
0
0
1
1
Benign
0
1
0
1
2
Conflicting
1
Total07417294

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

SYT10 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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Key Publications
Landmark & review papers · by relevance
PubMed
Top 5 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC