SYCE1

Chr 10AR

synaptonemal complex central element protein 1

Also known as: C10orf94, CT76, POF12, SPGF15

The protein is a major component of the synaptonemal complex central element that forms between homologous chromosomes during meiotic prophase and is required for chromosome synapsis initiation and elongation. Mutations cause premature ovarian failure 12 and spermatogenic failure 15, affecting reproductive function in both males and females. Inheritance is autosomal recessive.

OMIMResearchSummary from RefSeq, OMIM, UniProt
MultiplemechanismARLOEUF 0.962 OMIM phenotypes
Clinical SummarySYCE1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.96LOEUF
pLI 0.000
Z-score 1.69
OE 0.63 (0.420.96)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.66Z-score
OE missense 0.86 (0.760.98)
158 obs / 183.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.63 (0.420.96)
00.351.4
Missense OE0.86 (0.760.98)
00.61.4
Synonymous OE0.95
01.21.6
LoF obs/exp: 15 / 23.9Missense obs/exp: 158 / 183.3Syn Z: 0.33
DN
0.75top 25%
GOF
0.75top 25%
LOF
0.2190th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SYCE1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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