SYAP1

Chr X

synapse associated protein 1

Also known as: BSTA, PRO3113, SAP47

The SYAP1 protein promotes mTORC2-mediated phosphorylation of AKT1 and plays a role in adipocyte differentiation and cellular responses to growth factors. Mutations cause autosomal recessive neurodevelopmental disorders with intellectual disability and developmental delay. The gene is highly constrained against loss-of-function variants (pLI 0.94, LOEUF 0.35), indicating that complete loss of function is likely pathogenic.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.35
Clinical SummarySYAP1
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.94). One damaged copy is likely sufficient to cause disease.
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ClinVar Variants
7 unique Pathogenic / Likely Pathogenic· 14 VUS of 100 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.35LOEUF
pLI 0.943
Z-score 3.15
OE 0.07 (0.030.35)
Highly constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.16Z-score
OE missense 0.71 (0.600.85)
90 obs / 126.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.07 (0.030.35)
00.351.4
Missense OE0.71 (0.600.85)
00.61.4
Synonymous OE0.94
01.21.6
LoF obs/exp: 1 / 13.5Missense obs/exp: 90 / 126.7Syn Z: 0.34

ClinVar Variant Classifications

100 submitted variants in ClinVar

Classification Summary

Pathogenic7
VUS14
Likely Benign2
7
Pathogenic
14
VUS
2
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
7
0
7
Likely Pathogenic
0
0
0
0
0
VUS
0
14
0
0
14
Likely Benign
0
1
0
1
2
Benign
0
0
0
0
0
Total0157123

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

SYAP1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC