SUSD1

Chr 9

sushi domain containing 1

The protein functions as a cell surface receptor involved in cell adhesion and signaling processes. Mutations cause autosomal recessive intellectual disability with distinctive facial features and developmental delays. The gene shows low constraint against loss-of-function variants, consistent with the recessive inheritance pattern observed in affected individuals.

DNmechanismLOEUF 0.93
Clinical SummarySUSD1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.93LOEUF
pLI 0.000
Z-score 1.89
OE 0.67 (0.490.93)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.03Z-score
OE missense 0.86 (0.780.94)
349 obs / 407.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.67 (0.490.93)
00.351.4
Missense OE0.86 (0.780.94)
00.61.4
Synonymous OE1.02
01.21.6
LoF obs/exp: 26 / 38.7Missense obs/exp: 349 / 407.6Syn Z: -0.17
DN
0.6841th %ile
GOF
0.6346th %ile
LOF
0.2678th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SUSD1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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