SULT1B1

Chr 4

sulfotransferase family 1B member 1

Also known as: ST1B1, ST1B2, SULT1B2

SULT1B1 encodes a sulfotransferase enzyme that catalyzes sulfate conjugation of dopamine, thyroid hormones (T3 and reverse T3), and gut bacteria-derived metabolites that can affect brain myelination. The gene is not highly constrained against loss-of-function variants. Pathogenic variants in SULT1B1 have not been established as a cause of Mendelian disease.

OMIMResearchSummary from RefSeq, UniProt
MultiplemechanismLOEUF 1.31
Clinical SummarySULT1B1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.31LOEUF
pLI 0.000
Z-score 0.65
OE 0.82 (0.541.31)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.45Z-score
OE missense 1.10 (0.971.25)
172 obs / 156.3 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.82 (0.541.31)
00.351.4
Missense OE1.10 (0.971.25)
00.61.4
Synonymous OE1.25
01.21.6
LoF obs/exp: 13 / 15.8Missense obs/exp: 172 / 156.3Syn Z: -1.36
DN
0.7132th %ile
GOF
0.6542th %ile
LOF
0.2288th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SULT1B1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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