STK38L

Chr 12

serine/threonine kinase 38 like

Also known as: NDR2

The protein is a serine/threonine kinase that regulates structural processes in differentiating and mature neuronal cells and negatively regulates autophagy through protein phosphorylation pathways. Mutations cause neurodevelopmental disorders with intellectual disability, developmental delay, and neurological features. The gene shows autosomal recessive inheritance and is highly constrained against loss-of-function variants.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
4
Pubs (1 yr)
34
P/LP submissions
0%
P/LP missense
0.35
LOEUF· LoF intol.
Mechanism
Clinical SummarySTK38L
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.93). One damaged copy is likely sufficient to cause disease.
📋
ClinVar Variants
34 unique Pathogenic / Likely Pathogenic· 43 VUS of 104 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.35LOEUF
pLI 0.934
Z-score 4.03
OE 0.15 (0.070.35)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
2.94Z-score
OE missense 0.47 (0.410.55)
117 obs / 247.1 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.15 (0.070.35)
00.351.4
Missense OE0.47 (0.410.55)
00.61.4
Synonymous OE0.75
01.21.6
LoF obs/exp: 4 / 26.3Missense obs/exp: 117 / 247.1Syn Z: 1.74

ClinVar Variant Classifications

104 submitted variants in ClinVar

Classification Summary

Pathogenic33
Likely Pathogenic1
VUS43
Likely Benign8
Benign3
Conflicting2
33
Pathogenic
1
Likely Pathogenic
43
VUS
8
Likely Benign
3
Benign
2
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
33
0
33
Likely Pathogenic
0
0
1
0
1
VUS
0
31
12
0
43
Likely Benign
0
0
7
1
8
Benign
0
0
2
1
3
Conflicting
2
Total03155290

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

STK38L · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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Key Publications
Landmark & review papers · by relevance
PubMed
Top 3 results · since 2015Search PubMed ↗