STAT4

Chr 2AD

signal transducer and activator of transcription 4

Also known as: DPMC, SLEB11

STAT4 encodes a transcription factor that mediates responses to IL-12 and other cytokines, playing a critical role in T-helper cell differentiation and interferon-gamma production in immune responses. Mutations cause disabling pansclerotic morphea of childhood, a severe skin and connective tissue disorder, and increase susceptibility to systemic lupus erythematosus. The gene follows autosomal dominant inheritance and is highly constrained against loss-of-function variants.

OMIMResearchSummary from RefSeq, OMIM, UniProt
ADLOEUF 0.352 OMIM phenotypes
Clinical SummarySTAT4
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.77) — some intolerance to loss-of-function variants.
📋
ClinVar Variants
32 unique Pathogenic / Likely Pathogenic· 234 VUS of 569 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.35LOEUF
pLI 0.766
Z-score 5.15
OE 0.20 (0.130.35)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
2.74Z-score
OE missense 0.61 (0.550.68)
237 obs / 389.2 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.20 (0.130.35)
00.351.4
Missense OE0.61 (0.550.68)
00.61.4
Synonymous OE0.86
01.21.6
LoF obs/exp: 10 / 48.8Missense obs/exp: 237 / 389.2Syn Z: 1.25

ClinVar Variant Classifications

569 submitted variants in ClinVar

Classification Summary

Pathogenic30
Likely Pathogenic2
VUS234
Likely Benign257
Benign22
Conflicting6
30
Pathogenic
2
Likely Pathogenic
234
VUS
257
Likely Benign
22
Benign
6
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
1
29
0
30
Likely Pathogenic
0
1
1
0
2
VUS
8
201
21
4
234
Likely Benign
0
7
135
115
257
Benign
0
1
17
4
22
Conflicting
6
Total8211203123551

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

STAT4 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 5 results · since 2015Search PubMed ↗