ST3GAL3

Chr 1

ST3 beta-galactoside alpha-2,3-sialyltransferase 3

Also known as: DEE15, EIEE15, MRT12, SIAT6, ST3GALII, ST3Gal III, ST3GalIII, ST3N

The protein encoded by this gene is a type II membrane protein that catalyzes the transfer of sialic acid from CMP-sialic acid to galactose-containing substrates. The encoded protein is normally found in the Golgi apparatus but can be proteolytically processed to a soluble form. This protein is a member of glycosyltransferase family 29. Mutations in this gene have been associated with a form of autosomal recessive nonsymdromic cognitive disability as well as infantile epileptic encephalopathy. Multiple transcript variants encoding several different isoforms have been found for this gene. [provided by RefSeq, Jul 2017]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtIntellectual developmental disorder, autosomal recessive 12
UniProtDevelopmental and epileptic encephalopathy 15

Clinical highlights

Gene-disease validity (ClinGen)
complex neurodevelopmental disorder · ARModerateconsider for supplementary testing
0
Active trials
15
Pubs (1 yr)
P/LP submissions
P/LP missense
0.62
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.62LOEUF
pLI 0.003
Z-score 3.00
OE 0.36 (0.210.62)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
1.50Z-score
OE missense 0.74 (0.650.83)
188 obs / 255.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.36 (0.210.62)
00.351.4
Missense OE?0.74 (0.650.83)
00.61.4
Synonymous OE?0.97
01.21.6
LoF obs/exp: 9 / 25.3Missense obs/exp: 188 / 255.4Syn Z: 0.27

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ST3GAL3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →