SSNA1

Chr 9

SS nuclear autoantigen 1

Also known as: N14, NA-14, NA14

The protein stabilizes and protects microtubules from damage, induces microtubule branching, and is required for axon outgrowth and cell division. Mutations cause autosomal recessive cerebral palsy with spastic quadriplegia and intellectual disability. The gene shows tolerance to loss-of-function variants, suggesting the pathogenic variants may have different effects on protein function.

OMIMResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 1.83
Clinical SummarySSNA1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.83LOEUF
pLI 0.000
Z-score -0.10
OE 1.05 (0.541.83)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.60Z-score
OE missense 1.21 (1.011.45)
81 obs / 67.1 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.05 (0.541.83)
00.351.4
Missense OE1.21 (1.011.45)
00.61.4
Synonymous OE1.22
01.21.6
LoF obs/exp: 5 / 4.8Missense obs/exp: 81 / 67.1Syn Z: -0.96
DN
0.77top 25%
GOF
0.5170th %ile
LOF
0.3067th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SSNA1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗