SPSB4

Chr 3

splA/ryanodine receptor domain and SOCS box containing 4

Also known as: SSB-4, SSB4

Enables ubiquitin-like ligase-substrate adaptor activity. Involved in several processes, including positive regulation of protein polyubiquitination; protein ubiquitination; and ubiquitin-dependent protein catabolic process. Located in cytosol. [provided by Alliance of Genome Resources, Jul 2025]

OMIMResearchGenerating clinical summary…
LOEUF 1.41
Clinical SummarySPSB4
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
53 VUS of 56 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.41LOEUF
pLI 0.000
Z-score 0.74
OE 0.72 (0.391.41)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
0.87Z-score
OE missense 0.81 (0.700.94)
135 obs / 166.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.72 (0.391.41)
00.351.4
Missense OE?0.81 (0.700.94)
00.61.4
Synonymous OE?0.92
01.21.6
LoF obs/exp: 6 / 8.3Missense obs/exp: 135 / 166.6Syn Z: 0.54

ClinVar Variant Classifications

56 submitted variants in ClinVar

Classification Summary

VUS53
Likely Benign1
53
VUS
1
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
0
0
0
Likely Pathogenic
0
0
0
0
0
VUS
0
53
0
0
53
Likely Benign
0
1
0
0
1
Benign
0
0
0
0
0
Total0540054

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

22 pathogenic / likely-pathogenic (of 24) ClinVar copy-number / structural variants overlap SPSB4 — these span large chromosomal regions, not the gene specifically, and are excluded from the counts above. Explore in CNV tools →

Protein Context — Lollipop Plot

SPSB4 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →