SPSB3

Chr 16

splA/ryanodine receptor domain and SOCS box containing 3

Also known as: C16orf31, SSB3

SPSB3 encodes a substrate-recognition component of a cullin-5-RING E3 ubiquitin ligase complex that targets specific proteins for degradation, including nuclear cGAS and phosphorylated SNAI1. The gene is constrained against loss-of-function variants (LOEUF 0.71), but no Mendelian diseases have been definitively associated with SPSB3 mutations to date. Further research is needed to establish any clinical phenotypes and inheritance patterns associated with pathogenic variants in this gene.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.71
Clinical SummarySPSB3
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.34) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.71LOEUF
pLI 0.036
Z-score 2.37
OE 0.34 (0.170.71)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.78Z-score
OE missense 0.86 (0.770.96)
219 obs / 254.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.34 (0.170.71)
00.351.4
Missense OE0.86 (0.770.96)
00.61.4
Synonymous OE1.38
01.21.6
LoF obs/exp: 5 / 14.8Missense obs/exp: 219 / 254.2Syn Z: -3.16

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SPSB3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →