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SPG3A

Chr 14AD

spastic paraplegia 3A (autosomal dominant)

Also known as: AD-FSP, FSP1, SPG3

Atlastin-1 is a membrane-anchored GTPase that mediates GTP-dependent fusion of endoplasmic reticulum membranes, maintaining the continuous ER network and facilitating formation of three-way junctions where ER tubules intersect. Mutations cause spastic paraplegia 3A, an autosomal dominant hereditary spastic paraplegia that represents one of the most common early-onset forms of this condition. This gene has a GeneReviews entry, indicating established clinical guidelines are available for management.

OMIMResearchSummary from OMIM, UniProt
AD1 OMIM phenotype
Clinical SummarySPG3A
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Clinical Trials
2 active or recruiting trials — potential therapeutic options may be available
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/SPG3A?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SPG3A · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
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