SPATC1

Chr 8

spermatogenesis and centriole associated 1

Also known as: SPATA15

The SPATC1 protein binds gamma-tubulin and localizes to the centrosome, playing a role in microtubule organization. Mutations cause autosomal recessive spastic paraplegia with intellectual disability and seizures, typically presenting in early childhood. The gene shows minimal constraint against loss-of-function variants.

Summary from RefSeq
Research Assistant →
0
Active trials
0
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.25
LOEUF
Mechanism
Clinical SummarySPATC1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.25LOEUF
pLI 0.000
Z-score 0.76
OE 0.81 (0.541.25)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.06Z-score
OE missense 1.01 (0.931.10)
378 obs / 375.0 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.81 (0.541.25)
00.351.4
Missense OE1.01 (0.931.10)
00.61.4
Synonymous OE1.01
01.21.6
LoF obs/exp: 15 / 18.5Missense obs/exp: 378 / 375.0Syn Z: -0.07

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SPATC1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →