SPATA20

Chr 17

spermatogenesis associated 20

Also known as: HEL-S-98, SSP411, Tisp78

The protein is predicted to be involved in carbohydrate metabolism and cell differentiation and is located in mitochondria. Loss-of-function mutations in SPATA20 follow a de novo dominant inheritance pattern, though specific associated neurological diseases have not been established in the provided data. The extremely low pLI score suggests this gene is highly tolerant to loss-of-function variants.

Summary from RefSeq, UniProt, Mechanism
0
Active trials
4
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.70
LOEUF
DN
Mechanism· predicted
Clinical SummarySPATA20
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.70LOEUF
pLI 0.000
Z-score 3.18
OE 0.49 (0.350.70)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.12Z-score
OE missense 0.98 (0.911.06)
490 obs / 497.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.49 (0.350.70)
00.351.4
Missense OE0.98 (0.911.06)
00.61.4
Synonymous OE0.96
01.21.6
LoF obs/exp: 22 / 45.0Missense obs/exp: 490 / 497.7Syn Z: 0.42
DN
0.6745th %ile
GOF
0.5563th %ile
LOF
0.3066th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SPATA20 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC