SP140

Chr 2

SP140 nuclear body protein

Also known as: LYSP100, LYSP100-A, LYSP100-B

This gene encodes a member of the SP100 family of proteins, which are share common domains including an N-terminal homogeneously staining region domain followed by a SP100/autoimmune regulator/NucP41/P75/deformed epidermal autoregulatory factor domain, a plant homeobox zinc finger, and a bromodomain. The encoded protein is interferon-inducible and is expressed at high levels in the nuclei of leukocytes. Variants of this gene have been associated with multiple sclerosis, Crohn's disease, and chronic lymphocytic leukemia. Alternative splicing results in multiple variants. [provided by RefSeq, Aug 2016]

GeneReviewsResearchGenerating clinical summary…
0
Active trials
11
Pubs (1 yr)
P/LP submissions
P/LP missense
0.59
LOEUF
DN
Mechanism· predicted
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GeneReview available — SP140
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
0.59LOEUF
pLI 0.000
Z-score 4.00
OE 0.41 (0.290.59)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint?
0.79Z-score
OE missense 0.90 (0.820.97)
407 obs / 454.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.41 (0.290.59)
00.351.4
Missense OE?0.90 (0.820.97)
00.61.4
Synonymous OE?0.89
01.21.6
LoF obs/exp: 22 / 53.6Missense obs/exp: 407 / 454.2Syn Z: 1.12

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SP140 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →