SOX9CRE1

Chr 17AD

SOX9 enhancer cre1

This region represents an enhancer that is thought to regulate expression of the SRY-box 9 (SOX9) gene, located greater than 1 Mb downstream. This sequence is regulated by sonic hedgehog through binding by GLI family zinc finger 1. [provided by RefSeq, Jun 2016]

Primary Disease Associations & Inheritance

46XX sex reversal 2MIM #278850
AD
46XY sex reversal 10MIM #616425
AD
Acampomelic campomelic dysplasiaMIM #114290
AD
Campomelic dysplasiaMIM #114290
AD
Campomelic dysplasia with autosomal sex reversalMIM #114290
AD
0
Active trials
5
Pathogenic / LP
7
ClinVar variants
1
Pubs (1 yr)
Missense Z
LOEUF
Clinical SummarySOX9CRE1
📋
ClinVar Variants
5 Pathogenic / Likely Pathogenic· 1 VUS of 7 total submissions
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/SOX9CRE1?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

7 submitted variants in ClinVar

Classification Summary

Pathogenic5
VUS1
Likely Benign1
5
Pathogenic
1
VUS
1
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
5
Likely Pathogenic
0
VUS
1
Likely Benign
1
Benign
0
Total7

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

SOX9CRE1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →