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SOTOS

Chr 5AD

nuclear receptor binding SET domain protein 1

Also known as: ARA267, KMT3B, SOTOS, SOTOS1, STO

This gene encodes a transcriptional regulator containing a SET domain and multiple functional motifs that enhances androgen receptor transactivation and acts as a bifunctional transcriptional factor. Mutations cause Sotos syndrome, an autosomal dominant condition characterized by childhood overgrowth, macrocephaly, distinctive facial features, and developmental delays with onset in early childhood. The gene has also been associated with Weaver syndrome and is involved in certain cases of childhood acute myeloid leukemia through chromosomal translocations.

OMIMResearchSummary from RefSeq, OMIM
AD1 OMIM phenotype
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/SOTOS?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SOTOS · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Marybel Soto Gomez.
·New Phytol
2026
Sotos Syndrome
Adam MP et al.
2022
[Ricarte Soto Law, A Unique Case Study for Reflection].
Saldías-Fernández MA et al.·Rev Med Chil
2025
Sotos syndrome: A study of antenatal presentation.
Zhang YL et al.·Eur J Obstet Gynecol Reprod Biol
2022
Top 5 full-text resultsSearch PubTator3 ↗