SNAPIN

Chr 1AR

SNAP associated protein

Also known as: BLOC1S7, BLOS7, BORCS3, NEDBAC, SNAPAP

The protein encoded by this gene is a coiled-coil-forming protein that associates with the SNARE (soluble N-ethylmaleimide-sensitive fusion protein attachment protein receptor) complex of proteins and the BLOC-1 (biogenesis of lysosome-related organelles) complex. Biochemical studies have identified additional binding partners. As part of the SNARE complex, it is required for vesicle docking and fusion and regulates neurotransmitter release. The BLOC-1 complex is required for the biogenesis of specialized organelles such as melanosomes and platelet dense granules. Mutations in gene products that form the BLOC-1 complex have been identified in mouse strains that are models of Hermansky-Pudlak syndrome. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jun 2012]

OMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

Neurodevelopmental disorder with structural brain abnormalities and craniofacial abnormalitiesMIM #621393
AR
0
Active trials
14
Pubs (1 yr)
P/LP submissions
P/LP missense
1.44
LOEUF
Multiple*
Mechanism· predicted

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.44LOEUF
pLI 0.002
Z-score 0.77
OE 0.69 (0.361.44)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
0.88Z-score
OE missense 0.73 (0.590.90)
59 obs / 81.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.69 (0.361.44)
00.351.4
Missense OE?0.73 (0.590.90)
00.61.4
Synonymous OE?1.15
01.21.6
LoF obs/exp: 5 / 7.2Missense obs/exp: 59 / 81.3Syn Z: -0.69

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SNAPIN · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →