SNAPC4

Chr 9AR

small nuclear RNA activating complex polypeptide 4

Also known as: NEDRSO, PTFalpha, SNAP190

The protein is the largest subunit of the small nuclear RNA-activating protein (SNAPc) complex that binds to promoter elements and is essential for RNA polymerase II and III transcription of small nuclear RNA genes. Mutations cause ankylosing spondylitis, which follows autosomal dominant inheritance and primarily affects the spine and sacroiliac joints. The gene shows no significant constraint against loss-of-function variants.

OMIMResearchSummary from RefSeq, UniProt
LOFmechanismARLOEUF 0.981 OMIM phenotype
Clinical SummarySNAPC4
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.98LOEUF
pLI 0.000
Z-score 1.71
OE 0.78 (0.620.98)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
-1.08Z-score
OE missense 1.10 (1.041.16)
957 obs / 867.8 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.78 (0.620.98)
00.351.4
Missense OE1.10 (1.041.16)
00.61.4
Synonymous OE1.29
01.21.6
LoF obs/exp: 53 / 68.3Missense obs/exp: 957 / 867.8Syn Z: -4.51

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SNAPC4 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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