SNAP91

Chr 6

synaptosome associated protein 91

Also known as: AP180, CALM

The protein functions as a clathrin adaptor that links clathrin to receptors in coated vesicles and regulates clathrin-dependent endocytosis at synapses. Mutations cause autosomal recessive developmental and epileptic encephalopathy with movement abnormalities. This gene is extremely intolerant to loss-of-function variants, indicating that heterozygous variants are unlikely to be pathogenic in most cases.

OMIMResearchSummary from RefSeq, UniProt
LOFmechanismLOEUF 0.19
Clinical SummarySNAP91
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.19LOEUF
pLI 1.000
Z-score 5.44
OE 0.07 (0.030.19)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
2.16Z-score
OE missense 0.72 (0.650.79)
327 obs / 456.8 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.07 (0.030.19)
00.351.4
Missense OE0.72 (0.650.79)
00.61.4
Synonymous OE0.89
01.21.6
LoF obs/exp: 3 / 40.2Missense obs/exp: 327 / 456.8Syn Z: 1.16
DN
0.2997th %ile
GOF
0.3689th %ile
LOF
0.66top 25%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.19

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SNAP91 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found