SNAP29

Chr 22AR

synaptosome associated protein 29

The SNAP29 protein is a SNARE that mediates membrane fusion events, particularly autophagosome-lysosome fusion during autophagy and membrane fusions required for ciliogenesis. Biallelic mutations cause cerebral dysgenesis, neuropathy, ichthyosis, and palmoplantar keratoderma syndrome, a multisystem disorder affecting the brain, peripheral nerves, and skin with autosomal recessive inheritance. The gene shows tolerance to loss-of-function variants in the general population (high LOEUF score), suggesting complete loss of function may be required for disease manifestation.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 0.861 OMIM phenotype
Clinical SummarySNAP29
Population Constraint (gnomAD)
Low constraint (pLI 0.01) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.86LOEUF
pLI 0.014
Z-score 1.91
OE 0.41 (0.210.86)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
-0.87Z-score
OE missense 1.20 (1.061.36)
178 obs / 148.1 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.41 (0.210.86)
00.351.4
Missense OE1.20 (1.061.36)
00.61.4
Synonymous OE0.74
01.21.6
LoF obs/exp: 5 / 12.2Missense obs/exp: 178 / 148.1Syn Z: 1.52
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
strongSNAP29-related cerebral dysgenesis, neuropathy, ichthyosis, and palmoplantar keratoderma syndrome (CEDNIK syndrome)LOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.83top 10%
GOF
0.77top 25%
LOF
0.1697th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SNAP29 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →