SMIM20

Chr 4

small integral membrane protein 20

Also known as: C4orf52, MITRAC7, PNX

Involved in mitochondrial respiratory chain complex IV assembly. Located in mitochondrial inner membrane. [provided by Alliance of Genome Resources, Jun 2026]

OMIMResearchGenerating clinical summary…

Clinical highlights

Interpreting a novel variant
This gene is strongly intolerant of loss-of-function variation in the population, so LoF variants warrant close attention. No curated mechanism annotation is available — see the mechanism card for the computational prediction and its caveats.Based on population constraint only.
0
Active trials
6
Pubs (1 yr)
P/LP submissions
P/LP missense
1.10
LOEUF
DN
Mechanism· predicted

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
1.10LOEUF
pLI 0.575
Z-score 1.50
OE 0.00 (0.001.10)
Moderately constrained

Highly tolerant — LoF variants common in population

Missense Constraint?
0.63Z-score
OE missense 0.68 (0.480.98)
21 obs / 30.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.00 (0.001.10)
00.351.4
Missense OE?0.68 (0.480.98)
00.61.4
Synonymous OE?1.27
01.21.6
LoF obs/exp: 0 / 2.6Missense obs/exp: 21 / 30.8Syn Z: -0.76

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SMIM20 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →