SMIM12

Chr 1

small integral membrane protein 12

Also known as: C1orf212

SMIM12 encodes a small integral membrane protein located in the mitochondrion, though its specific functional role remains unclear. Mutations in this gene have been associated with neurodevelopmental disorders, but the clinical phenotype and inheritance pattern are not well-established in the current literature. This gene shows moderate constraint against loss-of-function variants.

ResearchSummary from RefSeq
GOFmechanismLOEUF 1.13
Clinical SummarySMIM12
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.57) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
1.13LOEUF
pLI 0.567
Z-score 1.48
OE 0.00 (0.001.13)
Moderately constrained

Highly tolerant — LoF variants common in population

Missense Constraint
1.20Z-score
OE missense 0.55 (0.420.74)
32 obs / 57.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.00 (0.001.13)
00.351.4
Missense OE0.55 (0.420.74)
00.61.4
Synonymous OE0.85
01.21.6
LoF obs/exp: 0 / 2.6Missense obs/exp: 32 / 57.7Syn Z: 0.57
DN
0.5673th %ile
GOF
0.6541th %ile
LOF
0.49top 25%

The highest-scoring mechanism for this gene is gain-of-function.

GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SMIM12 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found