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SMAPME

Chr 8AR

N-acylsphingosine amidohydrolase 1

Also known as: AC, ACDase, ASAH, PHP, PHP32, SMAPME

This gene encodes lysosomal acid ceramidase, which catalyzes the degradation of ceramide into sphingosine and free fatty acid. Mutations cause spinal muscular atrophy with progressive myoclonic epilepsy, a neuromuscular disorder affecting both the motor system and causing seizures. Inheritance is autosomal recessive.

GeneReviewsOMIMResearchSummary from RefSeq, OMIM
AR1 OMIM phenotype
📖
GeneReview available — SMAPME
Authoritative clinical overview · Recommended first read
Open GeneReview ↗
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/SMAPME?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SMAPME · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found