SLURP1

Chr 8AR

secreted LY6/PLAUR domain containing 1

Also known as: ANUP, ARS, ArsB, LY6-MT, LY6LS, MDM

The protein encoded by this gene is a member of the Ly6/uPAR family but lacks a GPI-anchoring signal sequence. It is thought that this secreted protein contains antitumor activity. Mutations in this gene have been associated with Mal de Meleda, a rare autosomal recessive skin disorder. This gene maps to the same chromosomal region as several members of the Ly6/uPAR family of glycoprotein receptors. [provided by RefSeq, Jul 2008]

Primary Disease Associations & Inheritance

Meleda diseaseMIM #248300
AR
UniProtMal de Meleda
0
Active trials
13
Pubs (1 yr)
88
P/LP submissions
11%
P/LP missense
1.31
LOEUF
LOF
Mechanism· G2P
Clinical SummarySLURP1
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.28) despite low pLI — interpret in context.
📋
ClinVar Variants
75 unique Pathogenic / Likely Pathogenic· 31 VUS of 118 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.31LOEUF
pLI 0.259
Z-score 1.24
OE 0.28 (0.101.31)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.59Z-score
OE missense 0.79 (0.641.00)
52 obs / 65.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.28 (0.101.31)
00.351.4
Missense OE0.79 (0.641.00)
00.61.4
Synonymous OE1.09
01.21.6
LoF obs/exp: 1 / 3.5Missense obs/exp: 52 / 65.5Syn Z: -0.38
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
definitiveSLURP1-related palmoplantar keratoderma transgrediens (Mal de Meleda)LOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.6356th %ile
GOF
0.6444th %ile
LOF
0.2386th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

118 submitted variants in ClinVar

Classification Summary

Pathogenic66
Likely Pathogenic9
VUS31
Likely Benign6
Benign3
Conflicting2
66
Pathogenic
9
Likely Pathogenic
31
VUS
6
Likely Benign
3
Benign
2
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
2
6
58
0
66
Likely Pathogenic
2
2
5
0
9
VUS
0
14
16
1
31
Likely Benign
0
0
3
3
6
Benign
0
0
2
1
3
Conflicting
2
Total422845117

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

SLURP1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC