SLITRK5

Chr 13

SLIT and NTRK like family member 5

Also known as: LRRC11, bA364G4.2

SLITRK5 encodes an integral membrane protein that suppresses neurite outgrowth and is expressed predominantly in neural tissues. Mutations cause Tourette syndrome and obsessive-compulsive disorder with autosomal dominant inheritance. The gene is highly constrained against loss-of-function variants (pLI = 0.87), indicating that complete loss of function is likely not tolerated.

OMIMResearchSummary from RefSeq, UniProt
MultiplemechanismLOEUF 0.38
Clinical SummarySLITRK5
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.87) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.38LOEUF
pLI 0.870
Z-score 3.81
OE 0.16 (0.080.38)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.05Z-score
OE missense 0.99 (0.931.07)
546 obs / 549.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.16 (0.080.38)
00.351.4
Missense OE0.99 (0.931.07)
00.61.4
Synonymous OE1.25
01.21.6
LoF obs/exp: 4 / 24.3Missense obs/exp: 546 / 549.5Syn Z: -3.08
DN
0.5477th %ile
GOF
0.6443th %ile
LOF
0.62top 25%

This gene has evidence for multiple mechanisms of pathogenicity (gain-of-function and loss-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to gain-of-function as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

GOFprediction above median
LOFLOEUF 0.38

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SLITRK5 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →