SLF2

Chr 10AR

SMC5/6 complex localization factor 2

Also known as: ATELS1, C10orf6, FAM178A, hNSE6

SLF2 encodes a protein that regulates DNA double-strand break repair by promoting recruitment of the SMC5-SMC6 DNA repair complex to sites of DNA damage and replication stress. Biallelic mutations cause Atelis syndrome 1, an autosomal recessive disorder characterized by genomic instability. The gene is highly constrained against loss-of-function variants (LOEUF 0.544), indicating that complete loss of protein function is poorly tolerated.

OMIMResearchSummary from RefSeq, OMIM, UniProt
ARLOEUF 0.541 OMIM phenotype
Clinical SummarySLF2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.54LOEUF
pLI 0.000
Z-score 4.17
OE 0.37 (0.260.54)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.97Z-score
OE missense 0.89 (0.830.95)
528 obs / 594.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.37 (0.260.54)
00.351.4
Missense OE0.89 (0.830.95)
00.61.4
Synonymous OE0.99
01.21.6
LoF obs/exp: 19 / 51.2Missense obs/exp: 528 / 594.6Syn Z: 0.07

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SLF2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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