SLCO1B3

Chr 12Digenic recessive

solute carrier organic anion transporter family member 1B3

Also known as: HBLRR, LST-2, LST-3TM13, LST3, OATP-8, OATP1B3, OATP8, SLC21A8

This gene encodes a liver-specific member of the organic anion transporter family. The encoded protein is a transmembrane receptor that mediates the sodium-independent uptake of endogenous and xenobiotic compounds and plays a critical role in bile acid and bilirubin transport. Mutations in this gene are a cause of Rotor type hyperbilirubinemia. Alternative splicing of this gene and the use of alternative promoters results in transcript variants encoding different isoforms that differ in their tissue specificity. [provided by RefSeq, Mar 2017]

GeneReviewsOMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

Hyperbilirubinemia, Rotor type, digenicMIM #237450
Digenic recessive
1
Active trials
37
Pubs (1 yr)
P/LP submissions
P/LP missense
1.54
LOEUF
Multiple*
Mechanism· predicted
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GeneReview available — SLCO1B3
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.54LOEUF
pLI 0.000
Z-score -0.77
OE 1.16 (0.881.54)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-1.16Z-score
OE missense 1.17 (1.081.27)
412 obs / 350.7 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?1.16 (0.881.54)
00.351.4
Missense OE?1.17 (1.081.27)
00.61.4
Synonymous OE?1.07
01.21.6
LoF obs/exp: 33 / 28.5Missense obs/exp: 412 / 350.7Syn Z: -0.61

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SLCO1B3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.