SLC5A5

Chr 19AR

solute carrier family 5 member 5

Also known as: NIS, TDH1

This gene encodes a member of the sodium glucose cotransporter family. The encoded protein is responsible for the uptake of iodine in tissues such as the thyroid and lactating breast tissue. The iodine taken up by the thyroid is incorporated into the metabolic regulators triiodothyronine (T3) and tetraiodothyronine (T4). Mutations in this gene are associated with thyroid dyshormonogenesis 1.[provided by RefSeq, Sep 2009]

GeneReviewsOMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

Thyroid dyshormonogenesis 1MIM #274400
AR

Clinical highlights

Interpreting a novel variant
Loss of function is the curated mechanism (Gene2Phenotype) and the gene is intolerant of it in the population — truncating, frameshift and canonical splice variants carry more prior weight here than missense.Curated gene-level mechanism — a prior for triage, not a per-variant call.
6
Active trials
31
Pubs (1 yr)
P/LP submissions
P/LP missense
0.56
LOEUF
LOF
Mechanism· G2P
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
0.56LOEUF
pLI 0.003
Z-score 3.39
OE 0.33 (0.200.56)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint?
0.92Z-score
OE missense 0.87 (0.790.95)
336 obs / 386.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.33 (0.200.56)
00.351.4
Missense OE?0.87 (0.790.95)
00.61.4
Synonymous OE?1.09
01.21.6
LoF obs/exp: 10 / 30.1Missense obs/exp: 336 / 386.8Syn Z: -0.96

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SLC5A5 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

Metastatic Thyroid Gland CarcinomaUnresectable Thyroid Gland Carcinoma

Dabrafenib and Lapatinib in Treating Patients With Refractory Thyroid Cancer That Cannot Be Removed by Surgery

ACTIVE NOT RECRUITING
NCT01947023Phase PHASE1National Cancer Institute (NCI)Started 2013-09-27
Biopsy ProcedureBiospecimen CollectionComputed Tomography
Fallopian Tube Clear Cell AdenocarcinomaFallopian Tube Endometrioid AdenocarcinomaFallopian Tube Mucinous Adenocarcinoma

MV-NIS Infected Mesenchymal Stem Cells in Treating Recurrent Ovarian, Primary Peritoneal or Fallopian Tube Cancer

ACTIVE NOT RECRUITING
NCT02068794Phase PHASE1, PHASE2Mayo ClinicStarted 2014-04-25
Laboratory Biomarker AnalysisMesenchymal Stem Cell TransplantationOncolytic Measles Virus Encoding Thyroidal Sodium Iodide Symporter
Peripheral T Cell LymphomaRelapsed Peripheral T-Cell LymphomaPeripheral T-Cell Lymphoma, Not Otherwise Specified

Intravenous Vesicular Stomatitis Virus in Patients With Peripheral T-cell Lymphoma

RECRUITING
NCT06508463Phase PHASE1Mayo ClinicStarted 2024-01-05
BiopsyBiospecimen CollectionBone Marrow Biopsy
Metastatic Endometrial CarcinomaRecurrent Endometrial AdenocarcinomaRecurrent Endometrial Carcinoma

VSV-hIFNbeta-NIS With or Without Ruxolitinib Phosphate in Treating Stage IV or Recurrent Endometrial Cancer

ACTIVE NOT RECRUITING
NCT03120624Phase PHASE1Mayo ClinicStarted 2017-09-15
BiopsyComputed TomographyFluorine F 18 Tetrafluoroborate
B-Cell Non-Hodgkin LymphomaHistiocytic and Dendritic Cell NeoplasmMyelodysplastic Syndrome

A Vaccine (VSV-hIFNβ-NIS) With or Without Cyclophosphamide and Combinations of Ipilimumab, Nivolumab, and Cemiplimab in Treating Relapsed or Refractory Multiple Myeloma, Acute Myeloid Leukemia or Lymphoma

RECRUITING
NCT03017820Phase PHASE1Mayo ClinicStarted 2017-04-04
Biopsy ProcedureBiospecimen CollectionBone Marrow Biopsy
Congenital Hypothyroidism

Role of Next Generation Sequencing in the Etiological Diagnosis of Permanent Congenital Hypothyroidism With in Situ Thyroid

RECRUITING
NCT06728735IRCCS Azienda Ospedaliero-Universitaria di BolognaStarted 2021-03-17