SLC38A3

Chr 3AR

solute carrier family 38 member 3

Also known as: DEE102, G17, NAT1, SN1, SNAT3

The SLC38A3 protein is a sodium-coupled amino acid transporter that cotransports glutamine, histidine, and asparagine across cell membranes and plays a critical role in the glutamate-GABA-glutamine cycle in the brain by facilitating glutamine uptake into neurons for neurotransmitter synthesis. Biallelic mutations cause developmental and epileptic encephalopathy 102, an autosomal recessive disorder affecting brain development and causing seizures. This condition primarily impacts the central nervous system through disruption of amino acid transport essential for normal neurotransmitter metabolism.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismAR1 OMIM phenotype

Population Genetics & Constraint

Constraint data not available from gnomAD.

Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
strongSLC38A3-related epileptic encephalopathyLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.6162th %ile
GOF
0.73top 25%
LOF
0.3647th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SLC38A3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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