SLC35C1

Chr 11AR

solute carrier family 35 member C1

Also known as: CDG2C, FUCT1

The protein functions as a GDP-fucose transporter in the Golgi apparatus, importing GDP-fucose from the cytoplasm into the Golgi lumen in exchange for GMP. Mutations cause congenital disorder of glycosylation type IIc, which follows autosomal recessive inheritance. This condition affects protein glycosylation and typically presents in infancy with developmental delays, seizures, and other multisystem manifestations.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 0.971 OMIM phenotype
Clinical SummarySLC35C1
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Gene-Disease Validity (ClinGen)
leukocyte adhesion deficiency type II · ARStrong

Strong evidence — appropriate for clinical testing

Population Constraint (gnomAD)
Low constraint (pLI 0.02) — loss-of-function variants are relatively tolerated in the population.
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Clinical Trials
2 active or recruiting trials — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.97LOEUF
pLI 0.024
Z-score 1.63
OE 0.43 (0.210.97)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.16Z-score
OE missense 0.78 (0.690.89)
172 obs / 220.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.43 (0.210.97)
00.351.4
Missense OE0.78 (0.690.89)
00.61.4
Synonymous OE1.13
01.21.6
LoF obs/exp: 4 / 9.4Missense obs/exp: 172 / 220.6Syn Z: -1.10
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
definitiveSLC35C1-related congenital disorder of glycosylationLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.76top 25%
GOF
0.75top 25%
LOF
0.2189th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SLC35C1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
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