SLC35B2

Chr 6

solute carrier family 35 member B2

Also known as: HLD26, PAPST1, SLL, UGTrel4

The SLC35B2 protein transports PAPS (3'-phosphoadenylyl sulfate) from the cytosol into the Golgi lumen, where it serves as the universal sulfate donor for sulfation of glycoproteins, proteoglycans, and glycolipids. Biallelic mutations cause autosomal recessive leukodystrophy, hypomyelinating, 26, with chondrodysplasia, affecting both the central nervous system and skeletal development. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.628).

ResearchSummary from RefSeq, OMIM, UniProt
DNmechanismLOEUF 0.63
Clinical SummarySLC35B2
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.30) despite low pLI — interpret in context.
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.63LOEUF
pLI 0.071
Z-score 2.66
OE 0.30 (0.150.63)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
-0.26Z-score
OE missense 1.05 (0.941.16)
263 obs / 251.4 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.30 (0.150.63)
00.351.4
Missense OE1.05 (0.941.16)
00.61.4
Synonymous OE1.29
01.21.6
LoF obs/exp: 5 / 16.7Missense obs/exp: 263 / 251.4Syn Z: -2.37
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
limitedSLC35B2-related chondrodysplasia with hypomyelinating leukodystrophyOTHERAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.7035th %ile
GOF
0.5856th %ile
LOF
0.3261th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SLC35B2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC