SLC24A5

Chr 15AR

solute carrier family 24 member 5

Also known as: JSX, NCKX5, OCA6, SHEP4

The protein functions as a calcium, potassium:sodium antiporter that transports calcium and potassium into melanosomes in exchange for cytoplasmic sodium, serving as the predominant sodium-calcium exchanger in melanocytes. Mutations cause oculocutaneous albinism type VI and variations in skin/hair/eye pigmentation, inherited in an autosomal recessive pattern. The gene shows high tolerance to loss-of-function variants (low constraint), consistent with its recessive inheritance pattern.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 1.162 OMIM phenotypes
Clinical SummarySLC24A5
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.16LOEUF
pLI 0.000
Z-score 0.97
OE 0.78 (0.531.16)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.32Z-score
OE missense 0.95 (0.851.05)
256 obs / 270.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.78 (0.531.16)
00.351.4
Missense OE0.95 (0.851.05)
00.61.4
Synonymous OE1.01
01.21.6
LoF obs/exp: 17 / 21.9Missense obs/exp: 256 / 270.7Syn Z: -0.06
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
definitiveSLC24A5-related albinism, oculocutaneousLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.76top 25%
GOF
0.74top 25%
LOF
0.2581th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SLC24A5 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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