SLC1A1

Chr 9

solute carrier family 1 member 1

Also known as: DCBXA, EAAC1, EAAT3, SCZD18, hEAAC1

This gene encodes a member of the high-affinity glutamate transporters that play an essential role in transporting glutamate across plasma membranes. In brain, these transporters are crucial in terminating the postsynaptic action of the neurotransmitter glutamate, and in maintaining extracellular glutamate concentrations below neurotoxic levels. This transporter also transports aspartate, and mutations in this gene are thought to cause dicarboxylicamino aciduria, also known as glutamate-aspartate transport defect. [provided by RefSeq, Mar 2010]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtDicarboxylic aminoaciduria
UniProtSchizophrenia 18

Clinical highlights

Gene-disease validity (ClinGen)
dicarboxylic aminoaciduria · ARLimitednot for standalone diagnostic reporting
0
Active trials
39
Pubs (1 yr)
P/LP submissions
P/LP missense
0.83
LOEUF
Multiple*
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.83LOEUF
pLI 0.000
Z-score 2.18
OE 0.51 (0.330.83)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
-1.33Z-score
OE missense 1.22 (1.121.33)
355 obs / 291.0 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.51 (0.330.83)
00.351.4
Missense OE?1.22 (1.121.33)
00.61.4
Synonymous OE?1.36
01.21.6
LoF obs/exp: 12 / 23.3Missense obs/exp: 355 / 291.0Syn Z: -2.99

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SLC1A1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →