SLC19A2

Chr 1

solute carrier family 19 member 2

Also known as: TC1, THMD1, THT1, THTR1, TRMA

This gene encodes the thiamin transporter protein. Mutations in this gene cause thiamin-responsive megaloblastic anemia syndrome (TRMA), which is an autosomal recessive disorder characterized by diabetes mellitus, megaloblastic anemia and sensorineural deafness. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Feb 2016]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtThiamine-responsive megaloblastic anemia syndrome
0
Active trials
23
Pubs (1 yr)
P/LP submissions
P/LP missense
0.76
LOEUF
Multiple*
Mechanism· predicted
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GeneReview available — SLC19A2
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.76LOEUF
pLI 0.000
Z-score 2.36
OE 0.44 (0.260.76)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.19Z-score
OE missense 0.97 (0.871.07)
263 obs / 271.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.44 (0.260.76)
00.351.4
Missense OE?0.97 (0.871.07)
00.61.4
Synonymous OE?0.96
01.21.6
LoF obs/exp: 9 / 20.6Missense obs/exp: 263 / 271.9Syn Z: 0.30

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SLC19A2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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