SHROOM3

Chr 4

shroom family member 3

This protein controls neuroepithelial cell shape changes during neural tube closure by promoting apical accumulation of F-actin and myosin II, and directing assembly of apicobasal microtubule arrays. Mutations cause neural tube defects including spina bifida and anencephaly, following an autosomal recessive inheritance pattern. The gene shows significant constraint against loss-of-function variants (LOEUF 0.35), reflecting its critical role in early nervous system development.

OMIMResearchSummary from RefSeq, UniProt
LOFmechanismLOEUF 0.35
Clinical SummarySHROOM3
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.23) despite low pLI — interpret in context.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.35LOEUF
pLI 0.317
Z-score 5.79
OE 0.23 (0.150.35)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.24Z-score
OE missense 0.90 (0.850.94)
1037 obs / 1155.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.23 (0.150.35)
00.351.4
Missense OE0.90 (0.850.94)
00.61.4
Synonymous OE0.92
01.21.6
LoF obs/exp: 15 / 65.6Missense obs/exp: 1037 / 1155.6Syn Z: 1.39

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SHROOM3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC