SFTPA1

Chr 10

surfactant protein A1

Also known as: COLEC4, ILD1, PSP-A, PSPA, SFTP1, SFTPA1B, SP-A, SP-A1

This gene encodes a lung surfactant protein that is a member of a subfamily of C-type lectins called collectins. The encoded protein binds specific carbohydrate moieties found on lipids and on the surface of microorganisms. This protein plays an essential role in surfactant homeostasis and in the defense against respiratory pathogens. Mutations in this gene are associated with idiopathic pulmonary fibrosis. Alternate splicing results in multiple transcript variants. [provided by RefSeq, May 2010]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtInterstitial lung disease 1
UniProtRespiratory distress syndrome in premature infants

Clinical highlights

Gene-disease validity (ClinGen)
interstitial lung disease 1 · ADModerateconsider for supplementary testing
0
Active trials
13
Pubs (1 yr)
P/LP submissions
P/LP missense
1.45
LOEUF
DN
Mechanism· predicted
📖
GeneReview available — SFTPA1
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.45LOEUF
pLI 0.000
Z-score 0.68
OE 0.74 (0.411.45)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.71Z-score
OE missense 1.16 (1.031.32)
173 obs / 148.5 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.74 (0.411.45)
00.351.4
Missense OE?1.16 (1.031.32)
00.61.4
Synonymous OE?1.00
01.21.6
LoF obs/exp: 6 / 8.1Missense obs/exp: 173 / 148.5Syn Z: -0.01

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SFTPA1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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