SFTA3

Chr 14

surfactant associated 3

Also known as: NANCI, PAHRF, SFTPH, SP-H, SPH

SFTA3 encodes a putative surfactant protein that may function in wound healing and reduction of surface tension at the ocular surface. The gene shows relatively low constraint to loss-of-function variation based on population genetics data. Currently, no definitive human diseases have been established from mutations in this gene.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
4
Pubs (1 yr)
203
P/LP submissions
16%
P/LP missense
0.96
LOEUF
GOF
Mechanism· predicted
Clinical SummarySFTA3
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.20) despite low pLI — interpret in context.
📋
ClinVar Variants
154 unique Pathogenic / Likely Pathogenic· 144 VUS of 406 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.96LOEUF
pLI 0.387
Z-score 1.63
OE 0.20 (0.070.96)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.57Z-score
OE missense 0.78 (0.601.01)
39 obs / 50.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.20 (0.070.96)
00.351.4
Missense OE0.78 (0.601.01)
00.61.4
Synonymous OE0.66
01.21.6
LoF obs/exp: 1 / 4.9Missense obs/exp: 39 / 50.3Syn Z: 1.22
DN
0.6164th %ile
GOF
0.76top 25%
LOF
0.3940th %ile

The highest-scoring mechanism for this gene is gain-of-function.

GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

406 submitted variants in ClinVar

Classification Summary

Pathogenic97
Likely Pathogenic57
VUS144
Likely Benign70
Benign14
Conflicting15
97
Pathogenic
57
Likely Pathogenic
144
VUS
70
Likely Benign
14
Benign
15
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
41
5
51
0
97
Likely Pathogenic
24
19
14
0
57
VUS
2
111
24
7
144
Likely Benign
0
3
15
52
70
Benign
0
1
11
2
14
Conflicting
15
Total6713911561397

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

SFTA3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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