SFRP2

Chr 4

secreted frizzled related protein 2

Also known as: FRP-2, SARP1, SDF-5

The protein functions as a soluble modulator of Wnt signaling through direct interaction with Wnt proteins and plays a role in eye retinal development and myogenesis. Mutations in this gene cause autosomal recessive retinal dystrophy with early childhood onset. The gene is not highly constrained against loss-of-function variants, consistent with a recessive inheritance pattern.

Summary from RefSeq, UniProt
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1
Active trials
80
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.06
LOEUF
DN
Mechanism· predicted
Clinical SummarySFRP2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
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Clinical Trials
1 active or recruiting trial — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.06LOEUF
pLI 0.002
Z-score 1.44
OE 0.54 (0.291.06)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
1.31Z-score
OE missense 0.71 (0.610.83)
119 obs / 166.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.54 (0.291.06)
00.351.4
Missense OE0.71 (0.610.83)
00.61.4
Synonymous OE1.25
01.21.6
LoF obs/exp: 6 / 11.2Missense obs/exp: 119 / 166.6Syn Z: -1.70
DN
0.6162th %ile
GOF
0.6052th %ile
LOF
0.2680th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SFRP2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Literature
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