SERPINA7

Chr XX-linked

serpin family A member 7

Also known as: TBG, TBGQTL

There are three proteins including thyroxine-binding globulin (TBG), transthyretin and albumin responsible for carrying the thyroid hormones thyroxine (T4) and 3,5,3'-triiodothyronine (T3) in the bloodstream. This gene encodes the major thyroid hormone transport protein, TBG, in serum. It belongs to the serpin family in genomics, but the protein has no inhibitory function like many other members of the serpin family. Mutations in this gene result in TGB deficiency, which has been classified as partial deficiency, complete deficiency, and excess, based on the level of serum TBG. Alternatively spliced transcript variants encoding different isoforms have been found, but the full-length nature of these variants has not been determined.[provided by RefSeq, Jun 2012]

GeneReviewsOMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

[Thyroxine-binding globulin QTL]MIM #300932
X-linked
[Thyroxine-binding globulin QTL]MIM #300932
X-linked
0
Active trials
12
Pubs (1 yr)
P/LP submissions
P/LP missense
1.27
LOEUF
Multiple*
Mechanism· predicted
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.27LOEUF
pLI 0.003
Z-score 1.06
OE 0.60 (0.311.27)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.66Z-score
OE missense 1.15 (1.021.31)
166 obs / 143.9 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.60 (0.311.27)
00.351.4
Missense OE?1.15 (1.021.31)
00.61.4
Synonymous OE?1.33
01.21.6
LoF obs/exp: 5 / 8.3Missense obs/exp: 166 / 143.9Syn Z: -1.93

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SERPINA7 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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