SCARF2

Chr 22AR

scavenger receptor class F member 2

SCARF2 encodes an adhesion protein that mediates cell-to-cell interactions and has limited scavenger receptor activity for modified lipoproteins. Biallelic mutations cause Van den Ende-Gupta syndrome, an autosomal recessive disorder characterized by distinctive craniofacial features, skeletal abnormalities, and developmental delays. The gene is highly constrained against loss-of-function variants (pLI 1.0, LOEUF 0.19), indicating intolerance to protein loss.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 0.191 OMIM phenotype
Clinical SummarySCARF2
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.19LOEUF
pLI 1.000
Z-score 5.01
OE 0.06 (0.020.19)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
3.02Z-score
OE missense 0.62 (0.560.68)
305 obs / 493.6 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.06 (0.020.19)
00.351.4
Missense OE0.62 (0.560.68)
00.61.4
Synonymous OE0.79
01.21.6
LoF obs/exp: 2 / 33.1Missense obs/exp: 305 / 493.6Syn Z: 2.55
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
definitiveSCARF2-related Van den Ende-Gupta syndromeLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.3395th %ile
GOF
0.6053th %ile
LOF
0.73top 10%

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SCARF2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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