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SCA40

Chr 14AD

coiled-coil and HOOK domain protein 88C

Also known as: DAPLE, HKRP2, HYC1, KIAA1509, SCA40

The encoded protein is a coiled-coil domain-containing protein that negatively regulates the Wnt signaling pathway through interaction with dishevelled protein. Mutations cause spinocerebellar ataxia 40, inherited in an autosomal dominant pattern. The gene is also associated with autosomal recessive congenital hydrocephalus, indicating its importance in cerebrospinal fluid regulation and cerebellar function.

OMIMResearchSummary from RefSeq, OMIM
LOFmechanismAD1 OMIM phenotype
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/SCA40?content-type=application/json&expand=1

gnomad: TimeoutError: The operation was aborted due to timeout

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SCA40 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC