SC5D

Chr 11AR

sterol-C5-desaturase

Also known as: ERG3, S5DES, SC5DL

This gene encodes an enzyme of cholesterol biosynthesis. The encoded protein catalyzes the conversion of lathosterol into 7-dehydrocholesterol. Mutations in this gene have been associated with lathosterolosis. Alternatively spliced transcript variants encoding the same protein have been described. [provided by RefSeq, Jul 2008]

GeneReviewsOMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

LathosterolosisMIM #607330
AR
0
Active trials
8
Pubs (1 yr)
P/LP submissions
P/LP missense
0.97
LOEUF
Multiple*
Mechanism· predicted
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GeneReview available — SC5D
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.97LOEUF
pLI 0.003
Z-score 1.66
OE 0.49 (0.270.97)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.72Z-score
OE missense 0.84 (0.730.97)
139 obs / 165.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.49 (0.270.97)
00.351.4
Missense OE?0.84 (0.730.97)
00.61.4
Synonymous OE?0.88
01.21.6
LoF obs/exp: 6 / 12.3Missense obs/exp: 139 / 165.1Syn Z: 0.75

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SC5D · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →