SAT2

Chr 17

spermidine/spermine N1-acetyltransferase family member 2

Also known as: SSAT-2, SSAT2

The protein catalyzes N-acetylation of thialysine and has weak activity toward polyamines like spermidine and spermine. SAT2 is highly constrained against loss-of-function variants (pLI near 1.0), but no established human disease has been definitively linked to SAT2 mutations in the medical literature. The gene follows autosomal inheritance patterns.

OMIMResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 1.55
Clinical SummarySAT2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.55LOEUF
pLI 0.000
Z-score 0.30
OE 0.90 (0.541.55)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.47Z-score
OE missense 0.87 (0.721.04)
84 obs / 97.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.90 (0.541.55)
00.351.4
Missense OE0.87 (0.721.04)
00.61.4
Synonymous OE0.89
01.21.6
LoF obs/exp: 9 / 10.0Missense obs/exp: 84 / 97.0Syn Z: 0.51
DN
0.7326th %ile
GOF
0.6249th %ile
LOF
0.2385th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

SAT2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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