RWDD2A

Chr 6

RWD domain containing 2A

Also known as: RWDD2, dJ747H23.2

The RWDD2A protein functions as a component of the CRL4-DDB1 ubiquitin ligase complex involved in protein degradation and DNA damage response. Mutations cause autosomal recessive developmental and epileptic encephalopathy with severe intellectual disability, seizures, and progressive microcephaly. The gene shows low constraint against loss-of-function variants, consistent with the recessive inheritance pattern observed in affected patients.

LOEUF 1.62
Clinical SummaryRWDD2A
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.62LOEUF
pLI 0.000
Z-score 0.08
OE 0.97 (0.601.62)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
1.07Z-score
OE missense 0.76 (0.650.88)
115 obs / 152.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.97 (0.601.62)
00.351.4
Missense OE0.76 (0.650.88)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 10 / 10.3Missense obs/exp: 115 / 152.3Syn Z: 0.01

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

RWDD2A · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found